Ectopia Lentis with Microspherophakia in Marfan Syndrome Resolved with Mydriasis
نویسندگان
چکیده
منابع مشابه
Bilateral ectopia lentis with isolated lens coloboma in Marfan syndrome
A rare case of bilateral ectopia lentis with isolated lens coloboma in Marfan syndrome is reported. A 21-year-old female presented with decreased vision in both eyes. Her unaided visual acuity was 20/200 and 20/400 in the right and left eye, respectively, improving to 20/40 with -4.5 DS/-3.0 DC x 10° correction in the right eye and 20/80 with -10.0 DS/-6.5 Dc x10° correction in the left eye. On...
متن کاملRetropupillary iris-claw intraocular lens in ectopia lentis in Marfan syndrome
OBJECTIVE To report visual outcomes, complication rate, and safety of retropupillary iris-claw intraocular lens (ICIOL) in ectopia lentis in Marfan syndrome (MFS). DESIGN Retrospective study. METHODS Six eyes of three MFS patients with ectopia lentis underwent surgery for subluxation lens and retropupillary ICIOL implantation from October 2014 to October 2015 at the Department of Ophthalmol...
متن کاملEctopia lentis as the presenting and primary feature in Marfan syndrome.
Marfan syndrome (MFS) is a multisystem connective tissue disorder with primary involvement of the ocular, cardiovascular, and skeletal systems. We report on eight patients, all presenting initially with bilateral ectopia lentis (EL) during early childhood. These individuals did not have systemic manifestations of MFS, and did not fulfill the revised Ghent diagnostic criteria. However, all patie...
متن کاملEctopia lentis et pupillae
The Ectopia lentis et pupillae is a rare genetic syndrome, congenital, autosomal recessive with variable expression, characterized by ectopia of the lens and the pupil, usually bilateral and symmetrical, but without systemic manifestations. The pathogenesis of this anomaly is still unknown, but there are theories that the change is mesodermal, neuroectodermal, combined or mechanical. This artic...
متن کاملEctopia lentis et pupillae syndrome in three generations.
In nine members from three generations and in a distant relative, at least three significant characteristics of the ectopia lentis et pupillae syndrome were established including ectopia lentis, ectopia pupillae, persistent pupillary membrane, iris transillumination, and poor pupillary dilatation. All patients developed bilateral cataract before the age of 40 years, and two patients presented w...
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ژورنال
عنوان ژورنال: Ophthalmology
سال: 2017
ISSN: 0161-6420
DOI: 10.1016/j.ophtha.2017.02.007